Torsed extralobar pulmonary sequestration associated with congenital lobar emphysema: a rare entity

作者全名："Wu, Yuhao; Xi, Linyun; Pan, Zhengxia; Wu, Chun; Li, Hongbo"

作者地址："[Wu, Yuhao; Xi, Linyun; Pan, Zhengxia; Wu, Chun; Li, Hongbo] Chongqing Med Univ, Dept Cardiothorac Surg, Childrens Hosp, Chongqing, Peoples R China; [Wu, Yuhao; Xi, Linyun; Pan, Zhengxia; Wu, Chun; Li, Hongbo] Minist Educ, Natl Clin Res Ctr Child Hlth & Disorders, Key Lab Child Dev & Disorders, Shanghai, Peoples R China"

通信作者："Li, HB (通讯作者)，Chongqing Med Univ, Dept Cardiothorac Surg, Childrens Hosp, Chongqing, Peoples R China.; Li, HB (通讯作者)，Minist Educ, Natl Clin Res Ctr Child Hlth & Disorders, Key Lab Child Dev & Disorders, Shanghai, Peoples R China."

来源：THERAPEUTIC ADVANCES IN RESPIRATORY DISEASE

ESI学科分类：CLINICAL MEDICINE

WOS号：WOS:000965802400001

JCR分区：Q2

影响因子：3.3

年份：2023

卷号：17

期号：　

开始页：　

结束页：　

文献类型：Article

关键词：children; pulmonary sequestration; torsion

摘要："Pulmonary sequestration (PS) is a rare congenital malformation, which mainly contains two variants involving extralobar and intralobar sequestrations. Extralobar sequestrations (ELS) are isolated from the remaining lung tissue and have their visceral pleura. Herein, we report the first case of a torsed ELS associated with congenital lobar emphysema. We described a boy who mainly presented with abdominal and chest pain. A contrast-enhanced computed tomography (CT) scan revealed a mildly enhanced posterior mediastinal mass with left lower lobar emphysema. Thoracoscopic surgery identified a dark and hemorrhagic mass that was connected to the thoracic aorta by a twisted feeding vessel and had its visceral pleura. Pathological findings were consistent with an ELS that had undergone torsion and infarction. The postoperative recovery was uneventful. For the left lower lobar emphysema, he was required for a regular outpatient follow-up. In conclusion, although extremely rare, physicians should maintain a high index of suspicion for torsed ELS when a posterior mediastinal mass with abdominal or chest pain is presented in children."

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