Hydroa vacciniforme-like lymphoproliferative disorder: A retrospective study on clinicopathological characteristics of 32 cases

作者全名："Xu, Wenfeng; Tan, Jingyi; Cai, Chenyu; Lei, Lei; Cao, Xian; Zhou, Hongling; Xu, Man"

作者地址："[Xu, Wenfeng; Cai, Chenyu; Lei, Lei; Cao, Xian; Zhou, Hongling; Xu, Man] Chongqing Med Univ, Mol Med & Canc Res Ctr, Dept Pathol, Chongqing, Peoples R China; [Tan, Jingyi] Chongqing Med Univ, Affiliated Hosp 1, Ctr Clin Mol Med Detect, Chongqin, Peoples R China"

通信作者："Xu, M (通讯作者)，Chongqing Med Univ, Mol Med & Canc Res Ctr, Dept Pathol, Chongqing, Peoples R China."

来源：PEDIATRIC DERMATOLOGY

ESI学科分类：CLINICAL MEDICINE

WOS号：WOS:000759204600001

JCR分区：Q3

影响因子：1.5

年份：2022

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期号：　

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文献类型：Article; Early Access

关键词：clinicopathological features; Epstein-Barr virus; hydroa vacciniforme; hydroa vacciniforme-like lymphoproliferative disorder; prognosis

摘要："The clinicopathological features of 32 patients (17 females and 15 males) with a median age of 8 years (range, 1.5-21 years) from Southwestern China diagnosed with hydroa vacciniforme-like lymphoproliferative disorder (HVLPD) were reviewed. At presentation, 6 patients showed only skin lesions, while 26 patients showed both skin lesions and systemic symptoms, including fever, lymphadenopathy and hepatosplenomegaly. As the disease progressed, systemic symptoms occurred in all patients. Follow-up data of 29 patients showed that 14 patients were still alive with disease with a median follow-up time of 22 months (range 3.6-71 months), and 15 patients died within a median follow-up of 6 months (range 0-60 months)."

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