A Giant Dendritic Fibromyxolipoma in the Right Thorax A Rare Entity

作者全名："Li, Hongbo; Zhu, Jin; Shen, Lianju; Pan, Zhengxia; Wu, Chun; Wu, Yuhao"

作者地址："[Li, Hongbo; Pan, Zhengxia; Wu, Chun; Wu, Yuhao] Chongqing Med Univ, Dept Cardiothorac Surg, Chongqing, Peoples R China; [Zhu, Jin] Chongqing Med Univ, Dept Pathol, Childrens Hosp, Chongqing, Peoples R China; [Li, Hongbo; Zhu, Jin; Shen, Lianju; Pan, Zhengxia; Wu, Chun; Wu, Yuhao] Minist Educ, Key Lab Child Dev & Disorders, Chongqing, Peoples R China; [Li, Hongbo; Zhu, Jin; Shen, Lianju; Pan, Zhengxia; Wu, Chun; Wu, Yuhao] Natl Clin Res Ctr Child Hlth & Disorders, Chongqing, Peoples R China; [Li, Hongbo; Zhu, Jin; Shen, Lianju; Pan, Zhengxia; Wu, Chun; Wu, Yuhao] China Int Sci & Technol Cooperat base Child Dev &, Chongqing, Peoples R China; [Li, Hongbo; Zhu, Jin; Shen, Lianju; Pan, Zhengxia; Wu, Chun; Wu, Yuhao] Chongqing Key Lab Pediat, Chongqing, Peoples R China"

通信作者："Wu, YH (通讯作者)，Chongqing Med Univ, Dept Cardiothorac Surg, Chongqing, Peoples R China.; Wu, YH (通讯作者)，Minist Educ, Key Lab Child Dev & Disorders, Chongqing, Peoples R China.; Wu, YH (通讯作者)，Natl Clin Res Ctr Child Hlth & Disorders, Chongqing, Peoples R China.; Wu, YH (通讯作者)，China Int Sci & Technol Cooperat base Child Dev &, Chongqing, Peoples R China.; Wu, YH (通讯作者)，Chongqing Key Lab Pediat, Chongqing, Peoples R China."

来源：CHEST

ESI学科分类：CLINICAL MEDICINE

WOS号：WOS:001092014700001

JCR分区：Q1

影响因子：9.6

年份：2023

卷号：164

期号：4

开始页：E89

结束页：E91

文献类型：Article

关键词：children; dendritic fi bromyxolipoma; tumor

摘要："Dendritic fibromyxolipoma (DFML) is an uncommon benign tumor. We report the first DFML in the right thorax of a child. An 11-year-old girl was admitted because of a giant tumor in the right thorax. An enhanced chest CT scan indicated a thoracic mass with mild enhancement. Thoracoscopic biopsy revealed that the tumor was composed of stellate and spindle cells embedded within abundant myxoid stroma. Additionally, mature adipocytes, cytoplasmic dendritic processes, short strands of keloidal-type collagen, and plexiform blood vessels were observed. Immunohistochemical staining indicated positive for CD34 and BCL-2. DDIT3 alteration or MDM2 amplification were not observed. The diagnosis of DFML was considered, and complete tumorectomy was performed. In conclusion, definite diagnosis of DFML should be made according to the pathologic features. Accurate diagnosis is crucial to avoid overtreatment because DFML potentially can be mistaken for more aggressive neoplasms."

基金机构："CQMU Program for Youth Innovation in Future Medicine, 2022 [W0204]"

基金资助正文："This study was funded by the CQMU Program for Youth Innovation in Future Medicine, 2022, W0204."